Pediatric Cardiology and Cardiac Surgery
Vol.24 No.2 2008 (93-98)

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Masahiro Kamada

Department of Pediatric Cardiology, Hiroshima City Hospital, Hiroshima, Japan


Any heart in which both great vessels arise entirely or predominantly from the right ventricle is considered to have double-outlet right ventricle (DORV). If more than half of the aorta is connected to the right ventricle in a patient with tetralogy of Fallot (ToF), the diagnosis of ToF with DORV can be made. The morphology of DORV is encompassed by a careful description of the ventricular septal defect with its relationship to the semilunar valves, the great arteries’ relationships to each other, coronary artery anatomy, the presence of pulmonary/aortic outflow tract obstruction, and other associated cardiac lesions. In this report the most common forms of DORV, those occurring with atrioventricular concordance, will be considered.