Pediatric Cardiology and Cardiac Surgery
Vol.24 No.2 2008 (93-98)
Department of Pediatric Cardiology, Hiroshima City Hospital, Hiroshima, Japan
Any heart in which both great vessels arise entirely or predominantly from the right ventricle is considered to have double-outlet right ventricle (DORV). If more than half of the aorta is connected to the right ventricle in a patient with tetralogy of Fallot (ToF), the diagnosis of ToF with DORV can be made. The morphology of DORV is encompassed by a careful description of the ventricular septal defect with its relationship to the semilunar valves, the great arteries’ relationships to each other, coronary artery anatomy, the presence of pulmonary/aortic outflow tract obstruction, and other associated cardiac lesions. In this report the most common forms of DORV, those occurring with atrioventricular concordance, will be considered.